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I42.2
ICD-10-CM
Hypertrophic Cardiomyopathy

Find comprehensive information on Hypertrophic Cardiomyopathy diagnosis, including clinical documentation, medical coding, ICD-10 codes (I42.1, I42.2), and SNOMED CT concepts. Learn about HCM diagnosis criteria, differential diagnosis, left ventricular hypertrophy, septal thickness, obstructive and nonobstructive HCM, genetic testing, echocardiography, and cardiac MRI for accurate healthcare documentation and coding compliance. Explore resources for physicians, clinicians, and coding professionals related to Hypertrophic Cardiomyopathy management.

Also known as

HCM
Idiopathic Hypertrophic Subaortic Stenosis
Asymmetric Septal Hypertrophy
+2 more

Diagnosis Snapshot

Key Facts
  • Definition : Heart muscle thickening, often in the septum, causing impaired outflow.
  • Clinical Signs : Shortness of breath, chest pain, syncope, palpitations, murmurs.
  • Common Settings : Primary care, cardiology clinic, inherited heart disease programs.

Related ICD-10 Code Ranges

Complete code families applicable to AAPC I42.2 Coding
I42.1-I42.2

Obstructive hypertrophic cardiomyopathy

Heart muscle thickening causing blockage of blood flow.

I42.0

Nonobstructive hypertrophic cardiomyop

Thickened heart muscle without flow obstruction.

I42.8

Other hypertrophic cardiomyopathies

Includes atypical hypertrophic cardiomyopathy.

I42.9

Hypertrophic cardiomyopathy, unspecified

Thickened heart muscle, type not specified.

Code-Specific Guidance

Decision Tree for

Follow this step-by-step guide to choose the correct ICD-10 code.

Is the cardiomyopathy obstructive?

  • Yes

    Is it familial?

  • No

    Is it familial?

Code Comparison

Related Codes Comparison

When to use each related code

Description
Heart muscle thickening
Athlete's heart
Hypertensive heart disease

Documentation Best Practices

Documentation Checklist
  • HCM diagnosis: Genetic testing results documented
  • HCM diagnosis: Echocardiogram findings detailed (LV wall thickness)
  • HCM diagnosis: Symptoms (e.g., dyspnea, chest pain) noted
  • HCM diagnosis: Family history of HCM recorded
  • HCM diagnosis: Differential diagnoses considered and ruled out

Coding and Audit Risks

Common Risks
  • Unspecified HCM Type

    Coding HCM without specifying obstructive or non-obstructive type (I42.1 vs. I42.2) leads to inaccurate severity reflection and reimbursement.

  • Missed Comorbidities

    Failing to code associated conditions like atrial fibrillation (I48.x) or heart failure (I50.x) impacts risk adjustment and resource allocation.

  • Lacking Supporting Documentation

    Insufficient clinical evidence in the medical record to support the HCM diagnosis (I42.x) exposes claims to denials and compliance issues.

Mitigation Tips

Best Practices
  • Document family history for accurate risk assessment. ICD-10 I42.1, I42.2
  • Echocardiogram is crucial for HCM diagnosis and severity grading. CPT 93306
  • Genetic testing clarifies diagnosis and family screening. CPT 81403
  • Detailed medication reconciliation for compliance and interactions.
  • Assess lifestyle factors for symptom management optimization.

Clinical Decision Support

Checklist
  • 1. Family Hx of HCM, SCD? ICD-10 I42.1, I42.2
  • 2. Unexplained LVH on echo? ICD-10 I42.1, R94.6
  • 3. Systolic anterior motion (SAM)? Document severity.
  • 4. Exclude other LVH causes (e.g., HTN). Doc. ddx

Reimbursement and Quality Metrics

Impact Summary
  • Hypertrophic Cardiomyopathy reimbursement hinges on accurate ICD-10-CM coding (I42.1, I42.2) and appropriate documentation of disease severity.
  • Quality metrics for HCM focus on appropriate diagnostic testing (ECG, echo) and therapy (beta-blockers, ICD implantation) impacting hospital reporting and pay-for-performance.
  • Coding errors for HCM (e.g., unspecified cardiomyopathy) can lead to claim denials and reduced reimbursement. Optimize coding for maximum revenue.
  • Proper documentation of HCM complications (e.g., atrial fibrillation, heart failure) impacts severity level and justifies higher reimbursement.

Streamline Your Medical Coding

Let S10.AI help you select the most accurate ICD-10 codes. Our AI-powered assistant ensures compliance and reduces coding errors.

Quick Tips

Practical Coding Tips
  • Code primary HCM diagnosis I42.1
  • Document LVH in echo report
  • Specify obstructive HCM with I42.0
  • Check for associated arrhythmia codes
  • Query physician for genetic HCM detail

Documentation Templates

Patient presents with symptoms suggestive of hypertrophic cardiomyopathy (HCM), including exertional dyspnea, chest pain, palpitations, and presyncope.  Family history is significant for sudden cardiac death, raising concern for genetic HCM.  Physical examination reveals a brisk carotid upstroke and a palpable fourth heart sound.  A systolic ejection murmur may be present, intensifying with Valsalva maneuver.  Electrocardiogram (ECG) demonstrates left ventricular hypertrophy (LVH) and repolarization abnormalities.  Transthoracic echocardiography (TTE) confirms the diagnosis of HCM, showing significant left ventricular wall thickening, typically involving the interventricular septum, with a left ventricular outflow tract (LVOT) gradient.  Differential diagnosis includes athlete's heart, hypertension with LVH, and other cardiomyopathies.  Cardiac magnetic resonance imaging (CMR) may be indicated for further evaluation of myocardial fibrosis and LVOT obstruction.  Genetic testing for HCM-associated mutations is recommended for the patient and potentially family members.  The patient's current New York Heart Association (NYHA) functional class is assessed.  Treatment plan includes beta-blockers or calcium channel blockers for symptom management and to reduce LVOT obstruction.  Surgical myectomy or alcohol septal ablation may be considered for patients with refractory symptoms despite optimal medical therapy.  Patient education focuses on lifestyle modifications, including avoiding strenuous exercise and dehydration, and recognizing symptoms of heart failure exacerbation.  Referral to a cardiologist specializing in HCM is warranted for ongoing management and risk stratification for sudden cardiac death.  ICD implantation may be indicated for high-risk individuals.  Regular follow-up is essential for monitoring disease progression and optimizing treatment strategies.
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