Find key clinical documentation and medical coding information for Interstitial Pulmonary Fibrosis IPF. Learn about IPF diagnosis codes, including ICD-10-CM codes J84.114 and J84.118, and relevant medical billing guidelines. Explore resources for accurate IPF documentation, pulmonary fibrosis staging, and healthcare provider guidelines for diagnosis and treatment. This resource offers valuable information for clinicians, coders, and healthcare professionals involved in IPF patient care.
Also known as
Interstitial pulmonary fibrosis
Scarring and thickening of lung tissue.
Other interstitial pulmonary diseases
Other specified interstitial lung conditions.
Interstitial pulmonary disease, unspecified
Interstitial lung disease without further specification.
Respiratory failure, not elsewhere classified
Lung failure not otherwise specified, a possible complication.
Follow this step-by-step guide to choose the correct ICD-10 code.
Is the diagnosis Idiopathic Pulmonary Fibrosis?
Yes
Code J84.110, Idiopathic pulmonary fibrosis
No
Is it another specified IPF?
When to use each related code
Description |
---|
Interstitial Pulmonary Fibrosis |
Hypersensitivity Pneumonitis |
Sarcoidosis |
Coding unspecified IPF (J84.1) when a more specific type is documented leads to inaccurate severity and resource reflection.
Missing documentation and coding of common IPF comorbidities like pulmonary hypertension or emphysema impacts risk adjustment.
Insufficient documentation of IPF progression stages (mild, moderate, severe) affects coding accuracy and quality reporting.
Patient presents with progressive dyspnea on exertion, a hallmark symptom of interstitial pulmonary fibrosis (IPF). The patient reports a persistent, dry, non-productive cough and exhibits inspiratory crackles on auscultation, consistent with pulmonary fibrosis symptoms. The patient denies fever, chills, or recent infections. The patient's medical history is significant for GERD, managed with omeprazole. Family history is negative for known genetic connective tissue disorders. Pulmonary function testing (PFT) reveals a restrictive pattern, characterized by reduced forced vital capacity (FVC) and total lung capacity (TLC), with a preserved FEV1FVC ratio. High-resolution computed tomography (HRCT) of the chest demonstrates bilateral, basal-predominant reticular opacities and honeycombing, characteristic of usual interstitial pneumonia (UIP) pattern, the radiologic hallmark of IPF. The patient's clinical presentation, PFT results, and HRCT findings meet the diagnostic criteria for IPF. Differential diagnosis included hypersensitivity pneumonitis, sarcoidosis, and chronic hypersensitivity pneumonitis, but these were ruled out based on clinical and radiographic findings. Treatment plan includes discussion of antifibrotic therapy (nintedanib or pirfenidone) to slow disease progression, pulmonary rehabilitation to improve exercise tolerance and quality of life, supplemental oxygen as needed for hypoxemia, and management of comorbidities. Patient education regarding prognosis, disease management, and the importance of follow-up care was provided. Referral to a pulmonary specialist for further evaluation and management is recommended. ICD-10 code J84.1, Idiopathic pulmonary fibrosis, is assigned. Medical billing codes will reflect evaluation and management services, pulmonary function testing, and HRCT chest.