Patient presents with symptoms suggestive of moderate pulmonary hypertension (PH), including dyspnea on exertion, fatigue, and chest pain.  Physical examination reveals elevated jugular venous pressure and a palpable right ventricular heave.  Auscultation identified a loud P2 heart sound and a tricuspid regurgitation murmur.  The patient's medical history includes a prior diagnosis of connective tissue disease.  Echocardiography demonstrates right ventricular hypertrophy and estimated pulmonary artery systolic pressure (PASP) between 40 and 55 mmHg, consistent with moderate PH (World Health Organization Group 1 pulmonary arterial hypertension, WHO Group 1 PAH).  Cardiac catheterization is planned for definitive hemodynamic assessment and to confirm the diagnosis of pulmonary arterial hypertension and exclude other causes of pulmonary hypertension such as WHO Group 2 PH due to left heart disease, WHO Group 3 PH due to lung diseases andor hypoxia, WHO Group 4 PH due to chronic thromboembolic disease, and WHO Group 5 PH with unclear or multifactorial mechanisms.  Differential diagnosis includes other causes of dyspnea and right heart failure.  Initial treatment plan includes diuretic therapy for symptom management and initiation of pulmonary arterial hypertension-specific therapy pending confirmation of diagnosis via right heart catheterization. Patient education provided regarding the disease process, medication management, lifestyle modifications including exercise limitations, and the importance of follow-up care.  Referral to a pulmonary hypertension specialist has been made.  ICD-10 code I27.21, Pulmonary hypertension, unspecified, is provisionally assigned, pending confirmatory testing.  CPT codes for evaluation and management, echocardiography, and upcoming right heart catheterization will be documented upon completion of those services. This documentation reflects current clinical practice guidelines for the diagnosis and management of pulmonary hypertension.