Facebook tracking pixel
D47.1
ICD-10-CM
Myeloproliferative Disorder

Find comprehensive information on Myeloproliferative Neoplasms MPN including clinical documentation requirements, ICD-10-CM diagnosis codes, medical coding guidelines, and healthcare resources for Essential Thrombocythemia ET, Polycythemia Vera PV, and Myelofibrosis MF. Learn about symptom management, treatment options, and prognosis for Myeloproliferative Disorders MPD. This resource provides valuable insights for healthcare professionals, coders, and patients seeking information on Myeloproliferative diseases.

Also known as

Myeloproliferative Neoplasm
MPN
Chronic Myeloproliferative Disease

Diagnosis Snapshot

Key Facts
  • Definition : Bone marrow disorders causing overproduction of blood cells, leading to thickened blood and complications.
  • Clinical Signs : Fatigue, enlarged spleen, night sweats, itching, easy bruising or bleeding, bone pain.
  • Common Settings : Hematology clinics, cancer centers, primary care (initial diagnosis).

Related ICD-10 Code Ranges

Complete code families applicable to AAPC D47.1 Coding
D47.1

Chronic myeloproliferative disorders

Group of disorders where bone marrow makes too many blood cells.

C92-C95

Myeloid and lymphoid neoplasms

Cancers affecting bone marrow and lymphatic system, sometimes overlapping.

D72-D72.9

Other disorders of blood and blood-forming organs

Catch-all for blood disorders not classified elsewhere, may include rare myeloproliferative diseases.

Code-Specific Guidance

Decision Tree for

Follow this step-by-step guide to choose the correct ICD-10 code.

Is the myeloproliferative disorder chronic myeloid leukemia (CML)?

  • Yes

    Code C92.1 for CML, chronic phase; C92.0 for CML, accelerated phase; C92.10 for CML, unspecified; C92.a1 for CML, blast crisis; C92.a2 for CML in remission

  • No

    Is it Polycythemia Vera?

Code Comparison

Related Codes Comparison

When to use each related code

Description
Overproduction of blood cells
Chronic blood cancer, high platelets
Bone marrow fibrosis, enlarged spleen

Documentation Best Practices

Documentation Checklist
  • Myeloproliferative disorder diagnosis documented
  • Bone marrow biopsy findings described
  • Genetic mutation analysis results (e.g., JAK2, CALR, MPL)
  • Complete blood count with differential reported
  • Presence or absence of splenomegaly documented

Coding and Audit Risks

Common Risks
  • Unspecified MDS Subtype

    Coding MDS without specifying subtype (e.g., using D47.9 instead of D47.1) leads to inaccurate DRG assignment and reimbursement.

  • MPN vs. MDS Overlap

    Misdiagnosis between MPN (D47.1) and MDS (D46.-) due to similar symptoms can impact quality metrics and treatment plans.

  • Missing JAK2 Mutation Status

    Failure to document JAK2 mutation status (positive/negative) for MPN affects risk stratification and treatment selection, impacting coding accuracy.

Mitigation Tips

Best Practices
  • Accurate ICD-10-CM coding (C92-C95) for MPD subtypes
  • Precise documentation of bone marrow biopsy findings for CDI
  • Regular monitoring of blood counts per NCCN guidelines for compliance
  • Genetic mutation testing (JAK2, CALR, MPL) clarifies MPD diagnosis
  • Risk stratification informs treatment and improves healthcare outcomes

Clinical Decision Support

Checklist
  • Review CBC: Elevated RBC, WBC, or platelets?
  • Check bone marrow biopsy: Hypercellularity?
  • JAK2, CALR, or MPL mutation analysis?
  • Assess for splenomegaly on physical exam?
  • Rule out reactive causes for blood cell elevation.

Reimbursement and Quality Metrics

Impact Summary
  • Myeloproliferative Disorder reimbursement: Coding accuracy impacts DRG assignment, affecting hospital case mix index.
  • Accurate ICD-10-CM coding (e.g., D47.1) for Myeloproliferative Neoplasms ensures appropriate reimbursement.
  • Quality metrics: Accurate coding reflects disease severity, impacting hospital quality reporting and pay-for-performance programs.
  • Timely and specific documentation of Myeloproliferative Disorder subtypes (e.g., ET, PV) improves coding and claims processing.

Streamline Your Medical Coding

Let S10.AI help you select the most accurate ICD-10 codes for . Our AI-powered assistant ensures compliance and reduces coding errors.

Quick Tips

Practical Coding Tips
  • Code primary myelofibrosis C94.1
  • Essential thrombocythemia D47.3
  • Polycythemia vera D45.1
  • Myeloproliferative neoplasm D47.1
  • Specify chronic or acute phase

Documentation Templates

Patient presents with symptoms suggestive of a myeloproliferative neoplasm (MPN).  Key findings include [Specify symptoms e.g., splenomegaly, fatigue, night sweats, weight loss, pruritus, bone pain, early satiety, abdominal fullness].  Complete blood count (CBC) reveals [Specify CBC findings e.g., elevated white blood cell count, elevated red blood cell count, elevated platelet count, presence of immature myeloid cells].  Peripheral blood smear shows [Specify findings e.g.,  anisopoikilocytosis, teardrop cells, nucleated red blood cells, left shift].  Bone marrow biopsy results indicate [Specify findings e.g., hypercellularity, increased megakaryocytes, reticulin fibrosis, JAK2 V617F mutation status].  Based on these findings, the diagnosis of myeloproliferative disorder is suspected, with a differential diagnosis including polycythemia vera, essential thrombocythemia, primary myelofibrosis, and chronic myeloid leukemia.  Further evaluation, including molecular testing for JAK2, CALR, and MPL mutations, is being performed to confirm the specific MPN subtype and guide treatment decisions.  Patient education regarding the nature of MPN, prognosis, and treatment options was provided.  Treatment plan will be determined based on the specific MPN subtype, disease risk stratification, and patient symptoms.  Potential treatment options include phlebotomy, low-dose aspirin, hydroxyurea, JAK2 inhibitors (e.g., ruxolitinib), and allogeneic stem cell transplantation.  Regular monitoring of blood counts, disease symptoms, and potential treatment complications will be essential.  ICD-10 code [Specify relevant ICD-10 code, e.g., D47.1] is being considered pending confirmatory testing.  Medical billing codes for evaluation and management, laboratory testing, and procedures performed will be documented accordingly.


 
Myeloproliferative Disorder - AI-Powered ICD-10 Documentation