Understand polycythemia vera diagnosis, clinical documentation, and medical coding. Find information on polycythemia rubra vera, JAK2 mutation testing, hematocrit levels, and complete blood count CBC interpretation. Learn about polycythemia treatment, management, and prognosis. Explore essential coding guidelines for polycythemia including ICD-10 codes D45 and related SNOMED CT concepts. This resource supports healthcare professionals in accurate diagnosis, documentation, and coding for polycythemia.
Also known as
Polycythemia vera
Bone marrow disorder causing overproduction of red blood cells.
Secondary polycythemia
Increased red blood cells due to another underlying condition.
Neonatal hemorrhage/hematological
Includes neonatal polycythemia and related blood disorders.
Follow this step-by-step guide to choose the correct ICD-10 code.
Is the polycythaemia due to a known underlying cause?
Yes
Due to hypoxia?
No
Is it Polycythaemia Vera (PV)?
When to use each related code
Description |
---|
High red blood cell count |
Essential thrombocythemia |
Myelofibrosis |
Coding polycythaemia without specifying vera/secondary creates HCC and CDI query risks impacting DRG assignment.
Failing to code thrombosis, myelofibrosis, or other related conditions with polycythaemia leads to underreporting severity and lost revenue.
Incorrectly sequencing polycythaemia as primary when it is secondary to another condition affects medical necessity and compliance.
Patient presents with symptoms suggestive of polycythemia vera, including headache, dizziness, pruritus, and erythromelalgia. Physical examination reveals splenomegaly and plethora. Complete blood count demonstrates elevated hemoglobin, hematocrit, and red blood cell count. White blood cell and platelet counts are also elevated. The patient denies any history of chronic hypoxia, carboxyhemoglobinemia, or erythropoietin-secreting tumors. Bone marrow biopsy shows hypercellularity with trilineage hyperplasia. JAK2 mutation analysis is pending. Differential diagnoses include secondary polycythemia and other myeloproliferative neoplasms. Assessment: Polycythemia vera, likely. Plan: Initiate phlebotomy to reduce hematocrit. Low-dose aspirin therapy will be started for thrombotic prophylaxis. Patient education provided regarding disease management, potential complications including thrombosis and transformation to myelofibrosis or acute myeloid leukemia, and the importance of follow-up appointments. Referral to hematology for further evaluation and management. ICD-10 code D45.1, Polycythemia vera, is assigned. Medical billing codes will reflect evaluation and management services, laboratory testing, and therapeutic phlebotomy. The patient will be scheduled for regular monitoring of blood counts, JAK2 mutation status, and assessment for disease progression.