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D86.9
ICD-10-CM
Sarcoidosis

Understanding Sarcoidosis diagnosis, symptoms, and treatment is crucial for accurate clinical documentation and medical coding. This resource provides information on Sarcoidosis ICD-10 codes, SNOMED CT codes, differential diagnosis, stages of Sarcoidosis, pulmonary Sarcoidosis, and extrapulmonary manifestations. Learn about the latest research, clinical trials, and best practices for managing Sarcoidosis in healthcare settings. Explore resources for patients, healthcare providers, and coding specialists seeking accurate and comprehensive information on Sarcoidosis.

Also known as

Besnier-Boeck disease
Boeck's sarcoid

Diagnosis Snapshot

Key Facts
  • Definition : Inflammatory disease forming granulomas in organs, commonly lungs and lymph nodes.
  • Clinical Signs : Cough, shortness of breath, fatigue, skin rashes, eye inflammation, joint pain.
  • Common Settings : Pulmonary clinics, rheumatology, ophthalmology, dermatology.

Related ICD-10 Code Ranges

Complete code families applicable to AAPC D86.9 Coding
D86.0-D86.9

Sarcoidosis

Covers all types and locations of sarcoidosis.

J98.3-J98.39

Respiratory conditions

Includes pulmonary sarcoidosis, affecting lungs.

K00-K93

Diseases of digestive system

May include sarcoidosis affecting digestive organs.

I00-I99

Diseases of the circulatory system

Can be used for cardiac sarcoidosis.

Code-Specific Guidance

Decision Tree for

Follow this step-by-step guide to choose the correct ICD-10 code.

Is sarcoidosis confirmed?

  • Yes

    Organ involvement specified?

  • No

    Do not code sarcoidosis. Code signs/symptoms or suspected diagnosis.

Code Comparison

Related Codes Comparison

When to use each related code

Description
Sarcoidosis: Inflammatory disease affecting multiple organs.
Hypersensitivity Pneumonitis: Lung inflammation due to inhaled antigens.
Tuberculosis: Infectious disease caused by Mycobacterium tuberculosis.

Documentation Best Practices

Documentation Checklist
  • Sarcoidosis diagnosis confirmed by biopsy
  • Organ involvement documented (e.g., lungs, skin)
  • Imaging findings consistent with sarcoidosis
  • Clinical presentation and symptoms detailed
  • Exclusion of other granulomatous diseases

Coding and Audit Risks

Common Risks
  • Unspecified Site Coding

    Coding sarcoidosis without specifying the affected organ system (e.g., lung, skin) leads to inaccurate data and reimbursement issues. Use specific ICD-10-CM codes (D86.0-D86.9).

  • Clinical Validation Deficit

    Lack of proper clinical documentation to support the sarcoidosis diagnosis can cause coding errors and compliance risks. CDI specialists must query for specificity.

  • Comorbidity Overcoding

    Incorrectly coding unrelated conditions as manifestations of sarcoidosis leads to inflated case complexity and potential fraud. Ensure accurate documentation links comorbidities.

Mitigation Tips

Best Practices
  • Thorough ICD-10-CM (D86.x) coding for sarcoidosis manifestations
  • Detailed clinical documentation of organ involvement for accurate CDI
  • Regular multidisciplinary review to optimize sarcoidosis management plans
  • Patient education on medication adherence & healthcare compliance
  • Timely follow-up & monitoring for disease progression & treatment response

Clinical Decision Support

Checklist
  • 1. Verify bilateral hilar lymphadenopathy on imaging (ICD-10: J98.89)
  • 2. Confirm noncaseating granulomas on biopsy (SNOMED: 422493008)
  • 3. Assess for elevated ACE levels (LOINC: 3094-0)
  • 4. Evaluate for extrapulmonary involvement (e.g., skin, eyes) (ICD-10: D86.89)

Reimbursement and Quality Metrics

Impact Summary
  • Sarcoidosis reimbursement hinges on accurate ICD-10-CM coding (D86.x) and supporting documentation for organ involvement.
  • Coding quality directly impacts Sarcoidosis case mix index (CMI) and hospital reimbursement levels.
  • Precise coding and staging are crucial for quality reporting initiatives regarding Sarcoidosis patient outcomes.
  • Physician documentation specificity is key for optimal Sarcoidosis reimbursement and accurate severity reflection.

Streamline Your Medical Coding

Let S10.AI help you select the most accurate ICD-10 codes. Our AI-powered assistant ensures compliance and reduces coding errors.

Quick Tips

Practical Coding Tips
  • Code D86.9 for unspecified sarcoidosis
  • Specify organ involvement with ICD-10-CM
  • Document confirmed diagnosis for Sarcoidosis
  • Use additional codes for manifestations
  • Query physician for unclear Sarcoidosis details

Documentation Templates

Patient presents with suspected sarcoidosis based on clinical presentation and preliminary investigations.  Symptoms include persistent cough, dyspnea, fatigue, and bilateral hilar lymphadenopathy observed on chest radiograph.  Differential diagnosis includes other granulomatous diseases such as tuberculosis, histoplasmosis, and lymphoma.  Pulmonary sarcoidosis is the primary working diagnosis given the patient's respiratory symptoms and radiological findings.  Further evaluation including pulmonary function tests, high-resolution computed tomography of the chest, and possible bronchoscopy with endobronchial ultrasound-guided transbronchial needle aspiration or biopsy is warranted to confirm the diagnosis and assess disease extent.  Serum angiotensin-converting enzyme levels and serum calcium levels will be obtained.  Patient education regarding sarcoidosis symptoms, staging, prognosis, and treatment options will be provided.  Treatment plan may involve corticosteroids, such as prednisone, or other immunosuppressants if indicated by disease severity and progression.  Patient will be monitored for treatment response and potential complications, including pulmonary fibrosis, cardiac involvement, ocular manifestations, and neurosarcoidosis.  Follow-up appointments will be scheduled to monitor disease activity and adjust treatment as needed.  ICD-10 code D86.9, sarcoidosis, unspecified, is the current presumptive diagnosis code.  This diagnosis may be updated pending further diagnostic testing results.  The medical decision-making complexity is currently moderate given the need to differentiate sarcoidosis from other granulomatous diseases.  This documentation supports medical necessity for the ordered tests and procedures.
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