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📖Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
D80-D89
Certain disorders involving the immune mechanism
Explore comprehensive insights into ICD-10 code range D80-D89, covering certain disorders involving the immune mechanism. Enhance clinical documentation accuracy and coding specificity with detailed guidelines for conditions like immunodeficiencies and autoimmune diseases. Perfect for healthcare professionals seeking to optimize patient records and improve billing accuracy.
About This Range
100+
Total codes
83+
Billable codes
17+
Non-billable
3
Chapters
Codes in this Range (100+)
Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism • Range: D50-D89
D80
Immunodeficiency with predominantly antibody defects
D80.0
Hereditary hypogammaglobulinemia
BillableD80.1
Nonfamilial hypogammaglobulinemia
BillableD80.2
Selective deficiency of immunoglobulin A [IgA]
BillableD80.3
Selective deficiency of immunoglobulin G [IgG] subclasses
BillableD80.4
Selective deficiency of immunoglobulin M [IgM]
BillableD80.5
Immunodeficiency with increased immunoglobulin M [IgM]
BillableD80.6
Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
BillableD80.7
Transient hypogammaglobulinemia of infancy
BillableD80.8
Other immunodeficiencies with predominantly antibody defects
BillableD80.9
Immunodeficiency with predominantly antibody defects, unspecified
BillableD81
Combined immunodeficiencies
D81.0
Severe combined immunodeficiency [SCID] with reticular dysgenesis
BillableD81.1
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
BillableD81.2
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
BillableD81.3
Adenosine deaminase [ADA] deficiency
D81.30
Adenosine deaminase deficiency, unspecified
BillableD81.31
Severe combined immunodeficiency due to adenosine deaminase deficiency
BillableD81.32
Adenosine deaminase 2 deficiency
BillableD81.39
Other adenosine deaminase deficiency
BillableD81.4
Nezelof's syndrome
BillableD81.5
Purine nucleoside phosphorylase [PNP] deficiency
BillableD81.6
Major histocompatibility complex class I deficiency
BillableD81.7
Major histocompatibility complex class II deficiency
BillableD81.8
Other combined immunodeficiencies
D81.81
Biotin-dependent carboxylase deficiency
D81.810
Biotinidase deficiency
BillableD81.818
Other biotin-dependent carboxylase deficiency
BillableD81.819
Biotin-dependent carboxylase deficiency, unspecified
BillableD81.82
Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
BillableD81.89
Other combined immunodeficiencies
BillableD81.9
Combined immunodeficiency, unspecified
BillableD82
Immunodeficiency associated with other major defects
D82.0
Wiskott-Aldrich syndrome
BillableD82.1
Di George's syndrome
BillableD82.2
Immunodeficiency with short-limbed stature
BillableD82.3
Immunodeficiency following hereditary defective response to Epstein-Barr virus
BillableD82.4
Hyperimmunoglobulin E [IgE] syndrome
BillableD82.8
Immunodeficiency associated with other specified major defects
BillableD82.9
Immunodeficiency associated with major defect, unspecified
BillableD83
Common variable immunodeficiency
D83.0
Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function
BillableD83.1
Common variable immunodeficiency with predominant immunoregulatory T-cell disorders
BillableD83.2
Common variable immunodeficiency with autoantibodies to B- or T-cells
BillableD83.8
Other common variable immunodeficiencies
BillableD83.9
Common variable immunodeficiency, unspecified
BillableD84
Other immunodeficiencies
D84.0
Lymphocyte function antigen-1 [LFA-1] defect
BillableD84.1
Defects in the complement system
BillableD84.8
Other specified immunodeficiencies
D84.81
Immunodeficiency due to conditions classified elsewhere
BillableD84.82
Immunodeficiency due to drugs and external causes
D84.821
Immunodeficiency due to drugs
BillableD84.822
Immunodeficiency due to external causes
BillableD84.89
Other immunodeficiencies
BillableD84.9
Immunodeficiency, unspecified
BillableD86
Sarcoidosis
D86.0
Sarcoidosis of lung
BillableD86.1
Sarcoidosis of lymph nodes
BillableD86.2
Sarcoidosis of lung with sarcoidosis of lymph nodes
BillableD86.3
Sarcoidosis of skin
BillableD86.8
Sarcoidosis of other sites
D86.81
Sarcoid meningitis
BillableD86.82
Multiple cranial nerve palsies in sarcoidosis
BillableD86.83
Sarcoid iridocyclitis
BillableD86.84
Sarcoid pyelonephritis
BillableD86.85
Sarcoid myocarditis
BillableD86.86
Sarcoid arthropathy
BillableD86.87
Sarcoid myositis
BillableD86.89
Sarcoidosis of other sites
BillableD86.9
Sarcoidosis, unspecified
BillableD89
Other disorders involving the immune mechanism, not elsewhere classified
D89.0
Polyclonal hypergammaglobulinemia
BillableD89.1
Cryoglobulinemia
BillableD89.2
Hypergammaglobulinemia, unspecified
BillableD89.3
Immune reconstitution syndrome
BillableD89.4
Mast cell activation syndrome and related disorders
D89.40
Mast cell activation, unspecified
BillableD89.41
Monoclonal mast cell activation syndrome
BillableD89.42
Idiopathic mast cell activation syndrome
BillableD89.43
Secondary mast cell activation
BillableD89.44
Hereditary alpha tryptasemia
BillableD89.49
Other mast cell activation disorder
BillableD89.8
Other specified disorders involving the immune mechanism, not elsewhere classified
D89.81
Graft-versus-host disease
D89.810
Acute graft-versus-host disease
BillableD89.811
Chronic graft-versus-host disease
BillableD89.812
Acute on chronic graft-versus-host disease
BillableD89.813
Graft-versus-host disease, unspecified
BillableD89.82
Autoimmune lymphoproliferative syndrome [ALPS]
BillableD89.83
Cytokine release syndrome
D89.831
Cytokine release syndrome, grade 1
BillableD89.832
Cytokine release syndrome, grade 2
BillableD89.833
Cytokine release syndrome, grade 3
BillableD89.834
Cytokine release syndrome, grade 4
BillableD89.835
Cytokine release syndrome, grade 5
BillableD89.839
Cytokine release syndrome, grade unspecified
BillableD89.84
IgG4-related disease
BillableD89.89
Other specified disorders involving the immune mechanism, not elsewhere classified
BillableD89.9
Disorder involving the immune mechanism, unspecified
BillablePeople also ask
Frequently Asked Questions
Primary immunodeficiency disorders, classified under ICD-10 codes D80-D89, often present with recurrent infections, chronic fatigue, and delayed growth in children. These symptoms occur due to the immune system's inability to effectively combat pathogens.
Diagnosis of immune mechanism disorders, such as those in the ICD-10 range D80-D89, typically involves a combination of blood tests to assess immune function, genetic testing, and clinical evaluation of symptoms. Early diagnosis is crucial for effective management.
Treatment for disorders involving the immune mechanism, covered under ICD-10 codes D80-D89, may include immunoglobulin replacement therapy, antibiotics for infection management, and in some cases, bone marrow transplantation. Treatment plans are tailored to individual patient needs.
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